Enfisema Lobar Congénito Caso 2. · · · fal jal. Congenital lobar emphysema (CLE) is a respiratory abnormality characterized by respiratory distress due to hyperinflation of one or more affected lobes of the. Request PDF on ResearchGate | Enfisema lobar congénito: Presentación de 4 casos | SUMMARY Congenital lobar emphysema is an unfrequent congenital.

Author: Mujora Mooguzil
Country: Iran
Language: English (Spanish)
Genre: Photos
Published (Last): 21 January 2014
Pages: 284
PDF File Size: 19.62 Mb
ePub File Size: 6.65 Mb
ISBN: 338-7-36393-662-1
Downloads: 21989
Price: Free* [*Free Regsitration Required]
Uploader: Tugore

Differential diagnosis Respiratory distress and radiolucency enfisema lobar congenito chest X rays can lead to a misdiagnosis of tension pneumothorax. Support Radiopaedia and see fewer ads. Thoracoscopic resection has been attempted and seems to have better post operative outcomes.

Enfisema Lobar Congénito

Case 10 Case Log in Sign up. Congenital lobar hyperinflation Infantile lobar hyperinflation Prevalence: Differential diagnoses also include congenital pulmonary airway malformation see conenito termpneumonia, bronchiolitis and foreign body aspiration.

Prompt diagnosis enfisema lobar congenito surgical intervention usually provide good long term outcome in symptomatic enfisema lobar congenito. CLO may be associated an aberrant left pulmonary artery 7 and also with congenital heart defects:. Case 6 Case 6. Case with hidden diagnosis.

Specialised Social Congdnito Eurordis directory.

Related articles Unilateral hypertranslucent hemithorax. For all other comments, please send your remarks via contact us.

Check for errors and try again. Patients with less severe manifestations may present in early childhood or rarely in adulthood. Diagnostic methods Chest X ray and CT scan are the key imaging modalities used for diagnosis. Key-words Congenital lobar enfisema lobar congenito. emfisema


Only comments written in English can be processed. Polyalveolar lobe has also been reported as a cause of CLE.

In the immediate postnatal period the affected lobe tends to appear opaque and homogeneous because of fetal lung fluid or it may show a diffuse reticular pattern enfisema lobar congenito represents distended lymphatic channels filled with fetal lung fluid. Chest radiographs demonstrates increased translucency of the left lung enfisema lobar congenito mild mediastinal shift to the right side.

Cases and figures Imaging differential diagnosis. Case 4 Case 4. Check this box lobbar you wish to receive a copy of your message.

Case 7 Case 7. Prenatal diagnosis can be made with ultrasonography enfisema lobar congenito identifying hyperechoic areas in fetal lung. On imaging, it classically presents on chest radiographs as a hyperlucent lung segment with overinflation and contralateral mediastinal shift. Synonyms enfisema lobar congenito Alternate Spellings: Most cases enfisema lobar congenito in the neonatal period or in early infancy.

Health care resources for this disease Expert centres 62 Diagnostic tests 0 Patient organisations 14 Orphan drug s 0. Mildly symptomatic patients are usually followed up. Case 11 Case Patients typically present with respiratory distress, most commonly in the neonatal period, and usually within the first six months of life 5. Congenital lobar emphysema CLE is a respiratory abnormality characterized by respiratory enfisema lobar congenito due to hyperinflation of one or more affected lobes of the lung.


Pediatric radiology, the requisites. Thank you for updating your details. About Blog Go ad-free. Only comments seeking to congrnito the quality and accuracy of information on congejito Orphanet website are accepted. Articles Cases Courses Quiz. Congenital lobar emphysema Case contributed by Dr Hani Salam. Recommended articles Citing articles 0.

Enfisema lobar congénito: Relato de caso – ScienceDirect

Abstract Congenital Lobar Emphysema CLE is a rare malformation of lung development, which may be the cause of respiratory insufficiency in the suckling child. Cojgenito despite the left upper lobe is most commonly affected, the right hemithorax is the most common side to be affected 6.

Echocardiography to detect concomitant heart enfisema lobar congenito can also be performed. Lobectomy of affected lobes is the widely accepted form of management with a satisfactory outcome.

What happens to the pulmonary vasculature in the affected lobe? Lobaf definition Congenital lobar emphysema CLE is a respiratory abnormality characterized by respiratory distress due to hyperinflation of one or more affected lobes of the lung. Lobectomy has better results than clinical treatment and should be chosen. Asymptomatic or mildly symptomatic cases can be managed conservatively but follow up is enfisema lobar congenito.

Case 8 Case 8. Most cases are idiopathic. Loading Stack – 0 images remaining.